Codon optimisation of microdystrophin improves expression and physiological outcome in dystrophic mdx mice following AAV2/8 gene transfer
Journal Article
Foster, H., Sharp, P., Trollet, C., Athanasopoulos, T., Graham, I., Foster, K., Wells, D. J., & Dickson, G. Codon optimisation of microdystrophin improves expression and physiological outcome in dystrophic mdx mice following AAV2/8 gene transfer. Molecular Therapy, 16(11), 1825-32. https://doi.org/10.1038/mt.2008.186
All Outputs (65)
Mice that overexpresses human heat shock protein 27 have increased renal injury following ischemia reperfusion
Journal Article
Chen, S. W. C., Kim, M., Kim, M., Song, J. H., Park, S. W., Wells, D. J., De Belleroche, J., D'Agati, V. C., & Lee, H. T. Mice that overexpresses human heat shock protein 27 have increased renal injury following ischemia reperfusion. Kidney International, 75(5), 499-510. https://doi.org/10.1038/ki.2008.572
Muscle moment arms and sensitivity analysis of a mouse hindlimb musculoskeletal model
Journal Article
Charles, J. P., Cappellari, O., Spence, A. J., Wells, D. J., & Hutchinson, J. R. (in press). Muscle moment arms and sensitivity analysis of a mouse hindlimb musculoskeletal model. Journal of Anatomy, 229(4), 514-535. https://doi.org/10.1111/joa.12461
Extracellular Release of the Atheroprotective Heat Shock Protein 27 Is Mediated by Estrogen and Competitively Inhibits acLDL Binding to Scavenger Receptor-A
Journal Article
Rayner, K., Chen, Y.-X., McNulty, M., Simard, T., Zhao, X., Wells, D. J., de Belleroche, J., & O'Brien, E. R. Extracellular Release of the Atheroprotective Heat Shock Protein 27 Is Mediated by Estrogen and Competitively Inhibits acLDL Binding to Scavenger Receptor-A. Circulation Research, 103(2), 133-141. https://doi.org/10.1161/CIRCRESAHA.108.172155
Protective effects of heat shock protein 27 in a model of ALS occur in the early stages of disease progression
Journal Article
Sharp, P. A., Akbar, T., Bouri, S., Senda, A., Joshi, K., Chen, H. J., Latchman, D. S., Wells, D. J., & De Belleroche, J. Protective effects of heat shock protein 27 in a model of ALS occur in the early stages of disease progression. Neurobiology of Disease, 30(1), 42-55. https://doi.org/10.1016/j.nbd.2007.12.002
Three-Dimensional Human iPSC-Derived Artificial Skeletal Muscles Model Muscular Dystrophies and Enable Multilineage Tissue Engineering
Journal Article
Maffioletti, S. M., Sarcar, S., Henderson, A. B. H., Mannhardt, I., Pinton, L., Moyle, L. A., Steele-Stallard, H., Cappellari, O., Wells, K. E., Ferrari, G., Mitchell, J. S., Tyzack, G. E., Kotiadis, V. N., Khedr, M., Ragazzi, M., Wang, W., Duchen, M. R., Patani, R., Zammit, P. S., Wells, D. J., …Tedesco, F. S. (in press). Three-Dimensional Human iPSC-Derived Artificial Skeletal Muscles Model Muscular Dystrophies and Enable Multilineage Tissue Engineering. Cell Reports, 23(3), 899-908. https://doi.org/10.1016/j.celrep.2018.03.091
Effect of albumin and dextrose concentration on ultrasound and microbubble mediated gene transfection in vivo
Journal Article
Browning, R. J., Mulvana, H., Tang, M. X., Hajnal, J. V., Wells, D. J., & Eckersley, R. J. Effect of albumin and dextrose concentration on ultrasound and microbubble mediated gene transfection in vivo. Ultrasound in Medicine and Biology, 38(6), 1067-77. https://doi.org/10.1016/j.ultrasmedbio.2012.02.020
Influence of needle gauge on in vivo ultrasound and microbubble-mediated gene transfection
Journal Article
Browning, R. J., Mulvana, H., Tang, M. X., Hajnal, J. V., Wells, D. J., & Eckersley, R. J. Influence of needle gauge on in vivo ultrasound and microbubble-mediated gene transfection. Ultrasound in Medicine and Biology, 37(9), 1531-1537. https://doi.org/10.1016/j.ultrasmedbio.2011.05.019
Investigation of a transgenic mouse model of familial dilated cardiomyopathy
Journal Article
Song, W., Dyer, E., Stuckey, D., Leung, M.-C., Memo, M., Mansfield, C., Ferenczi, M., Liu, K., Redwood, C., Nowak, K., Harding, S., Clarke, K., Wells, D. J., & Marston, S. Investigation of a transgenic mouse model of familial dilated cardiomyopathy. Journal of Molecular and Cellular Cardiology, 49(3), 380-389. https://doi.org/10.1016/j.yjmcc.2010.05.009
Microbubble stability is a major determinant of the efficiency of ultrasound and microbubble mediated in vivo gene transfer
Journal Article
Alter, J., Sennoga, C. A., Lopes, D., Eckserley, R. J., & Wells, D. J. Microbubble stability is a major determinant of the efficiency of ultrasound and microbubble mediated in vivo gene transfer. Ultrasound in Medicine and Biology, 35(6), 976-84. https://doi.org/10.1016/j.ultrasmedbio.2008.12.015
Systemic MV Gene Therapy Close to Clinical Trials for Several Neuromuscular Diseases
Journal Article
Wells, D. J. (in press). Systemic MV Gene Therapy Close to Clinical Trials for Several Neuromuscular Diseases. Molecular Therapy, 25(4), 834-835. https://doi.org/10.1016/j.ymthe.2017.03.006
Designing translationally relevant preclinical studies of new therapeutics
Journal Article
Wells, D. J. Designing translationally relevant preclinical studies of new therapeutics. Experimental Physiology, 102(6), 616. https://doi.org/10.1113/EP086296
Determination of qPCR Reference Genes Suitable for Normalizing Gene Expression in a Canine Model of Duchenne Muscular Dystrophy
Journal Article
Hildyard, J. C. W., Taylor-Brown, F. E., Massey, C., Wells, D. J., & Piercy, R. J. (in press). Determination of qPCR Reference Genes Suitable for Normalizing Gene Expression in a Canine Model of Duchenne Muscular Dystrophy. Journal of Neuromuscular Diseases, 5(2), 177-191. https://doi.org/10.3233/JND-170267Background:Dogs with dystrophin-deficient muscular dystrophy are valuable models of the equivalent human disease, Duchenne Muscular Dystrophy (DMD): unlike the mdx mouse, these animals present a disease severity and progression that closely matches t... Read More about Determination of qPCR Reference Genes Suitable for Normalizing Gene Expression in a Canine Model of Duchenne Muscular Dystrophy.
Characterisation of the pathogenic effects of the in vivo expression of an ALS-linked mutation in D-amino acid oxidase: Phenotype and loss of spinal cord motor neurons
Journal Article
Kondori, N. R., Paul, P., Robbins, J. P., Liu, K., Hildyard, J. C. W., Wells, D. J., & De Belleroche, J. S. (in press). Characterisation of the pathogenic effects of the in vivo expression of an ALS-linked mutation in D-amino acid oxidase: Phenotype and loss of spinal cord motor neurons. PLoS ONE, 12, e0188912. https://doi.org/10.1371/journal.pone.0188912Amyotrophic lateral sclerosis (ALS) is the most common adult-onset neuromuscular disorder characterised by selective loss of motor neurons leading to fatal paralysis. Current therapeutic approaches are limited in their effectiveness. Substantial adva... Read More about Characterisation of the pathogenic effects of the in vivo expression of an ALS-linked mutation in D-amino acid oxidase: Phenotype and loss of spinal cord motor neurons.
Molecular Mechanism of the E99K Mutation in Cardiac Actin (ACTC Gene) That Causes Apical Hypertrophy in Man and Mouse
Journal Article
Song, W., Dyer, E., Stuckey, D. J., Copeland, O., Leung, M. C., Bayliss, C., Messer, A., Wilkinson, R., Tremoleda, J. L., Schneider, M. D., Harding, S. E., Redwood, C. S., Clarke, K., Nowak, K., Monserrat, L., Wells, D. J., & Marston, S. B. (in press). Molecular Mechanism of the E99K Mutation in Cardiac Actin (ACTC Gene) That Causes Apical Hypertrophy in Man and Mouse. Journal of Biological Chemistry, 286(31), 27582–27593. https://doi.org/10.1074/jbc.M111.252320
Histopathological Evaluation of Skeletal Muscle with Specific Reference to Mouse Models of Muscular Dystrophy
Journal Article
Terry, R. L., & Wells, D. J. Histopathological Evaluation of Skeletal Muscle with Specific Reference to Mouse Models of Muscular Dystrophy. https://doi.org/10.1002/cpmo.19
Olfaction variation in mouse husbandry and its implications for refinement and standardization: UK survey of animal scents
Journal Article
Lopez-Salesansky, N., Mazlan, N. H., Whitfield, L. E., Wells, D. J., & Burn, C. C. (in press). Olfaction variation in mouse husbandry and its implications for refinement and standardization: UK survey of animal scents. Laboratory Animals, 50(5), 362-369. https://doi.org/10.1177/0023677215622883
Implications for Cardiac Function Following Rescue of the Dystrophic Diaphragm in a Mouse Model of Duchenne Muscular Dystrophy
Journal Article
Betts, C. A., Saleh, A. F., Carr, C. A., Muses, S., Wells, K. E., Hammond, S. M., Godfrey, C., McClorey, G., Woffindale, C., Clarke, K., Wells, D. J. G. M. J., & Wood, M. J. A. (in press). Implications for Cardiac Function Following Rescue of the Dystrophic Diaphragm in a Mouse Model of Duchenne Muscular Dystrophy. https://doi.org/10.1038/srep11632
In silico characterisation and chromosomal localisation of human RRH (peropsin) – implications for opsin evolution
Journal Article
Bellingham, J., Wells, D. J., & Foster, R. G. In silico characterisation and chromosomal localisation of human RRH (peropsin) – implications for opsin evolution. BMC Genomics, 4(1), 3. https://doi.org/10.1186/1471-2164-4-3
Improving translational studies: lessons from rare neuromuscular diseases
Journal Article
Wells, D. J. Improving translational studies: lessons from rare neuromuscular diseases. Disease Models and Mechanisms, 8(10), 1175-7. https://doi.org/10.1242/dmm.022616