Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease) (2016)
Journal Article
Wager, K., Zdebik, A. A., Fu, S., Cooper, J. D., Harvey, R. J., & Russell, C. (2016). Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease). PLoS ONE, 11(6), https://doi.org/10.1371/journal.pone.0157365

The neuronal ceroid lipofuscinoses are a group of lysosomal storage disorders that comprise the most common, genetically heterogeneous, fatal neurodegenerative disorders of children. They are characterised by childhood onset, visual failure, epilepti... Read More about Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease).

Granulin Knock Out Zebrafish Lack Frontotemporal Lobar Degeneration and Neuronal Ceroid Lipofuscinosis Pathology (2015)
Journal Article
Solchenberger, B., Russell, C., Kremmer, E., Haass, C., & Schmid, B. (2015). Granulin Knock Out Zebrafish Lack Frontotemporal Lobar Degeneration and Neuronal Ceroid Lipofuscinosis Pathology. PLoS ONE, 10(3), https://doi.org/10.1371/journal.pone.0118956

The compound BTB06584 is an IF1-dependent selective inhibitor of the mitochondrial F1Fo-ATPase (2014)
Journal Article
Ivanes, F., Faccenda, D., Gatliff, J., Ahmed, A. A., Cocco, S., Cheng, C. H. K., …Campanella, M. (2014). The compound BTB06584 is an IF1-dependent selective inhibitor of the mitochondrial F1Fo-ATPase. British Journal of Pharmacology, 171(18), 4193-4206. https://doi.org/10.1111/bph.12638

Epilepsy research methods update: Understanding the causes of epileptic seizures and identifying new treatments using non-mammalian model organisms
Journal Article
Cunliffe, V. T., Baines, R. A., Giachello, C. N. G., Lin, W., Morgan, A., Reuber, M., …Williams, R. S. B. Epilepsy research methods update: Understanding the causes of epileptic seizures and identifying new treatments using non-mammalian model organisms. https://doi.org/10.1016/j.seizure.2014.09.018

VALPROIC ACID EXTENDS LIFESPAN OF THE ZEBRAFISH MODEL OF CLN2 DISEASE (LATE INFANTILE NEURONAL CEROID LIPOFUSCINOSIS)
Journal Article
Mahmood, F., Zdebik, A., Au, A., Cooke, J., & Russell, C. VALPROIC ACID EXTENDS LIFESPAN OF THE ZEBRAFISH MODEL OF CLN2 DISEASE (LATE INFANTILE NEURONAL CEROID LIPOFUSCINOSIS). https://doi.org/10.1136/jnnp-2015-312379.61

Modelling Inborn Errors of Metabolism in Zebrafish
Conference Proceeding
Wager, K., Mahmood, F., & Russell, C. Modelling Inborn Errors of Metabolism in Zebrafish. https://doi.org/10.1007/s10545-014-9696-5

Generation and validation of a zebrafish model of EAST (Epilepsy, Ataxia, Sensorineural deafness and Tubulopathy) syndrome
Journal Article
Mahmood, F., Kaminskaite, M., Zdebik, A. A., Stanescu, H. C., Tobin, J., Beales, P. L., …Russell, C. Generation and validation of a zebrafish model of EAST (Epilepsy, Ataxia, Sensorineural deafness and Tubulopathy) syndrome. Disease Models and Mechanisms, 6(3), 652. https://doi.org/10.1242/dmm.009480

A zebrafish model of CLN2 disease is deficient in Tripeptidyl-peptidase I and displays progressive neurodegeneration accompanied by a reduction in proliferation
Journal Article
Russell, C., Mahmood, F., Fu, S., Cooke, J., Wilson, S., & Cooper, J. A zebrafish model of CLN2 disease is deficient in Tripeptidyl-peptidase I and displays progressive neurodegeneration accompanied by a reduction in proliferation. Brain, 136, 1488. https://doi.org/10.1093/brain/awt043

Mitophagy and neurodegeneration The zebrafish model system
Journal Article
Wager, K., & Russell, C. Mitophagy and neurodegeneration The zebrafish model system. Autophagy, 9(11), 1693-1709. https://doi.org/10.4161/auto.25082

Epilepsy in kcnj10 Morphant Zebrafish Assessed with a Novel Method for Long-Term EEG Recordings
Journal Article
Zdebik, A. A., Mahmood, F., Stanescu, H. C., Kleta, R., Bockenhauer, D., & Russell, C. Epilepsy in kcnj10 Morphant Zebrafish Assessed with a Novel Method for Long-Term EEG Recordings. PLoS ONE, 8(11), https://doi.org/10.1371/journal.pone.0079765